Síndrome de Mayer-Rokitansky- Küster-Hauser. Reporte de dos casos.

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Title: Síndrome de Mayer-Rokitansky- Küster-Hauser. Reporte de dos casos.
Alternate Title: Mayer-Rokitansky-Küster-Hauser Syndrome: Two cases report.
Authors: Ávila-Vergara, Marco Antonio1 mavila_v@uas.edu.mx, León-Álvarez, Damián Alfredo2, López-Villegas, Miriam Nayeli2, Quintero-Medrano, Samantha Melissa2, Angulo-Bueno, Gladys Fabiola2, Vadillo-Ortega, Felipe3
Source: Ginecología y Obstetricia de México. mar2015, Vol. 83 Issue 3, p199-205. 7p. 5 Black and White Photographs.
Subjects: MAYER-Rokitansky-Kuster-Hauser syndrome, PRIMARY amenorrhea, UTERUS abnormalities, SCOLIOSIS, DIAGNOSTIC ultrasonic imaging, ABDOMINAL surgery, PATIENTS, THERAPEUTICS
Abstract (English): Agenesia of the Müllerian ducts is a low-frequency congenital disease but with devastating effects on women's reproductive health. In this paper we present two cases of women affected by Mayer-Rokitansky-Küster-Hauser syndrome (MRKH). First case was a 17-year-old woman with aplasia of the upper vagina and absence of uterus. No other defects were found and was classified as type 1-MRKH. Second case was 18-year-old woman with absence of uterus, escoliosis and polycystic ovary syndrome, classified as type II-MRKH. Patients were seen at the Hospital with primary amenorrhea and fully developed secondary sexual characteristics. A clinical follow-up protocol, including the use of high-resolution image studies was used for diagnosis. Diagnostic procedures and current medical approaches to the treatment of MRKH are discussed, including psychological advisory, surgical procedures and new tissue-engineering techniques. [ABSTRACT FROM AUTHOR]
Abstract (Spanish): La agenesia de los conductos de Müller es un padecimiento congénito poco frecuente pero de gran afectación. Se comunican dos casos de pacientes con síndrome de Mayer-Rokitansky-Küster-Hauser. El primer caso correspondió a una mujer de 17 años de edad con síndrome tipo 1, con aplasia de los dos tercios superiores de la vagina y ausencia de útero, sin otras alteraciones asociadas. El segundo caso es de una mujer de 18 años de edad con síndrome tipo 2 en la que se documentó ausencia de útero, escoliosis y síndrome de ovario poliquístico. El motivo de consulta fue: amenorrea primaria con desarrollo completo de characteres sexuales secundarios en ambos casos. Se utilizó un protocolo clínico para descartar diagnósticos diferenciales y se estableció el diagnóstico con ayuda de imagenología de alta resolución. Se discuten los procedimientos diagnósticos y tratamientos médicos actuales: atención psicológica, intervenciones quirúrgicas y técnicas de ingeniería de tejidos para formación de la neovagina. [ABSTRACT FROM AUTHOR]
Copyright of Ginecología y Obstetricia de México is the property of Federacion Mexicana de Ginecologia y Obstetricia and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract. (Copyright applies to all Abstracts.)
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Items – Name: Title
  Label: Title
  Group: Ti
  Data: Síndrome de Mayer-Rokitansky- Küster-Hauser. Reporte de dos casos.
– Name: TitleAlt
  Label: Alternate Title
  Group: TiAlt
  Data: Mayer-Rokitansky-Küster-Hauser Syndrome: Two cases report.
– Name: Author
  Label: Authors
  Group: Au
  Data: <searchLink fieldCode="AR" term="%22Ávila-Vergara%2C+Marco+Antonio%22">Ávila-Vergara, Marco Antonio</searchLink><relatesTo>1</relatesTo><i> mavila_v@uas.edu.mx</i><br /><searchLink fieldCode="AR" term="%22León-Álvarez%2C+Damián+Alfredo%22">León-Álvarez, Damián Alfredo</searchLink><relatesTo>2</relatesTo><br /><searchLink fieldCode="AR" term="%22López-Villegas%2C+Miriam+Nayeli%22">López-Villegas, Miriam Nayeli</searchLink><relatesTo>2</relatesTo><br /><searchLink fieldCode="AR" term="%22Quintero-Medrano%2C+Samantha+Melissa%22">Quintero-Medrano, Samantha Melissa</searchLink><relatesTo>2</relatesTo><br /><searchLink fieldCode="AR" term="%22Angulo-Bueno%2C+Gladys+Fabiola%22">Angulo-Bueno, Gladys Fabiola</searchLink><relatesTo>2</relatesTo><br /><searchLink fieldCode="AR" term="%22Vadillo-Ortega%2C+Felipe%22">Vadillo-Ortega, Felipe</searchLink><relatesTo>3</relatesTo>
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  Data: <searchLink fieldCode="JN" term="%22Ginecología+y+Obstetricia+de+México%22">Ginecología y Obstetricia de México</searchLink>. mar2015, Vol. 83 Issue 3, p199-205. 7p. 5 Black and White Photographs.
– Name: Subject
  Label: Subjects
  Group: Su
  Data: <searchLink fieldCode="DE" term="%22MAYER-Rokitansky-Kuster-Hauser+syndrome%22">MAYER-Rokitansky-Kuster-Hauser syndrome</searchLink><br /><searchLink fieldCode="DE" term="%22PRIMARY+amenorrhea%22">PRIMARY amenorrhea</searchLink><br /><searchLink fieldCode="DE" term="%22UTERUS+abnormalities%22">UTERUS abnormalities</searchLink><br /><searchLink fieldCode="DE" term="%22SCOLIOSIS%22">SCOLIOSIS</searchLink><br /><searchLink fieldCode="DE" term="%22DIAGNOSTIC+ultrasonic+imaging%22">DIAGNOSTIC ultrasonic imaging</searchLink><br /><searchLink fieldCode="DE" term="%22ABDOMINAL+surgery%22">ABDOMINAL surgery</searchLink><br /><searchLink fieldCode="DE" term="%22PATIENTS%22">PATIENTS</searchLink><br /><searchLink fieldCode="DE" term="%22THERAPEUTICS%22">THERAPEUTICS</searchLink>
– Name: Abstract
  Label: Abstract (English)
  Group: Ab
  Data: Agenesia of the Müllerian ducts is a low-frequency congenital disease but with devastating effects on women's reproductive health. In this paper we present two cases of women affected by Mayer-Rokitansky-Küster-Hauser syndrome (MRKH). First case was a 17-year-old woman with aplasia of the upper vagina and absence of uterus. No other defects were found and was classified as type 1-MRKH. Second case was 18-year-old woman with absence of uterus, escoliosis and polycystic ovary syndrome, classified as type II-MRKH. Patients were seen at the Hospital with primary amenorrhea and fully developed secondary sexual characteristics. A clinical follow-up protocol, including the use of high-resolution image studies was used for diagnosis. Diagnostic procedures and current medical approaches to the treatment of MRKH are discussed, including psychological advisory, surgical procedures and new tissue-engineering techniques. [ABSTRACT FROM AUTHOR]
– Name: Abstract
  Label: Abstract (Spanish)
  Group: Ab
  Data: La agenesia de los conductos de Müller es un padecimiento congénito poco frecuente pero de gran afectación. Se comunican dos casos de pacientes con síndrome de Mayer-Rokitansky-Küster-Hauser. El primer caso correspondió a una mujer de 17 años de edad con síndrome tipo 1, con aplasia de los dos tercios superiores de la vagina y ausencia de útero, sin otras alteraciones asociadas. El segundo caso es de una mujer de 18 años de edad con síndrome tipo 2 en la que se documentó ausencia de útero, escoliosis y síndrome de ovario poliquístico. El motivo de consulta fue: amenorrea primaria con desarrollo completo de characteres sexuales secundarios en ambos casos. Se utilizó un protocolo clínico para descartar diagnósticos diferenciales y se estableció el diagnóstico con ayuda de imagenología de alta resolución. Se discuten los procedimientos diagnósticos y tratamientos médicos actuales: atención psicológica, intervenciones quirúrgicas y técnicas de ingeniería de tejidos para formación de la neovagina. [ABSTRACT FROM AUTHOR]
– Name: AbstractSuppliedCopyright
  Label:
  Group: Ab
  Data: <i>Copyright of Ginecología y Obstetricia de México is the property of Federacion Mexicana de Ginecologia y Obstetricia and its content may not be copied or emailed to multiple sites without the copyright holder's express written permission. Additionally, content may not be used with any artificial intelligence tools or machine learning technologies. However, users may print, download, or email articles for individual use. This abstract may be abridged. No warranty is given about the accuracy of the copy. Users should refer to the original published version of the material for the full abstract.</i> (Copyright applies to all Abstracts.)
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RecordInfo BibRecord:
  BibEntity:
    Languages:
      – Code: spa
        Text: Spanish
    PhysicalDescription:
      Pagination:
        PageCount: 7
        StartPage: 199
    Subjects:
      – SubjectFull: MAYER-Rokitansky-Kuster-Hauser syndrome
        Type: general
      – SubjectFull: PRIMARY amenorrhea
        Type: general
      – SubjectFull: UTERUS abnormalities
        Type: general
      – SubjectFull: SCOLIOSIS
        Type: general
      – SubjectFull: DIAGNOSTIC ultrasonic imaging
        Type: general
      – SubjectFull: ABDOMINAL surgery
        Type: general
      – SubjectFull: PATIENTS
        Type: general
      – SubjectFull: THERAPEUTICS
        Type: general
    Titles:
      – TitleFull: Síndrome de Mayer-Rokitansky- Küster-Hauser. Reporte de dos casos.
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            NameFull: Ávila-Vergara, Marco Antonio
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            NameFull: León-Álvarez, Damián Alfredo
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            NameFull: López-Villegas, Miriam Nayeli
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            NameFull: Quintero-Medrano, Samantha Melissa
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            NameFull: Angulo-Bueno, Gladys Fabiola
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            NameFull: Vadillo-Ortega, Felipe
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              Text: mar2015
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              Y: 2015
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