Changes in peak oxygen consumption in Fabry disease and associations with cardiomyopathy severity.

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Title: Changes in peak oxygen consumption in Fabry disease and associations with cardiomyopathy severity.
Authors: Roy A; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK ashwinroy@nhs.net.; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK., Thompson SE; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK., Hodson J; University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK., van Vliet J; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK., Condon N; Department of Inherited Metabolic Diseases, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK., Alvior AM; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK., O'Shea C; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK., Vijapurapu R; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Cardiology, Queen Elizabeth Hospital, Birmingham, UK., Nightingale TE; University of Birmingham, Birmingham, UK., Clift PF; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Grown Up Congenital Heart Disease Unit, Queen Elizabeth Hospital, Birmingham, UK., Townend J; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Cardiology, Queen Elizabeth Hospital, Birmingham, UK., Geberhiwot T; Endocrinology, Queen Elizabeth Hospital, Birmingham, UK.; University of Birmingham Institute of Metabolism and Systems Research, Birmingham, UK., Steeds RP; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Cardiology, Queen Elizabeth Hospital, Birmingham, UK.
Source: Heart (British Cardiac Society) [Heart] 2025 Feb 12; Vol. 111 (5), pp. 230-238. Date of Electronic Publication: 2025 Feb 12.
Publication Type: Journal Article; Observational Study
Journal Info: Publisher: BMJ Pub. Group Country of Publication: England NLM ID: 9602087 Publication Model: Electronic Cited Medium: Internet ISSN: 1468-201X (Electronic) Linking ISSN: 13556037 NLM ISO Abbreviation: Heart Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Changes in peak oxygen consumption in Fabry disease and associations with cardiomyopathy severity.
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  Data: <searchLink fieldCode="AU" term="%22Roy+A%22">Roy A</searchLink>; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK ashwinroy@nhs.net.; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Thompson+SE%22">Thompson SE</searchLink>; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Hodson+J%22">Hodson J</searchLink>; University Hospitals Birmingham NHS Foundation Trust, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22van+Vliet+J%22">van Vliet J</searchLink>; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Condon+N%22">Condon N</searchLink>; Department of Inherited Metabolic Diseases, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Alvior+AM%22">Alvior AM</searchLink>; Department of Cardiology, University Hospital Birmingham NHS Foundation Trust, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22O'Shea+C%22">O'Shea C</searchLink>; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Vijapurapu+R%22">Vijapurapu R</searchLink>; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Cardiology, Queen Elizabeth Hospital, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Nightingale+TE%22">Nightingale TE</searchLink>; University of Birmingham, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Clift+PF%22">Clift PF</searchLink>; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Grown Up Congenital Heart Disease Unit, Queen Elizabeth Hospital, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Townend+J%22">Townend J</searchLink>; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Cardiology, Queen Elizabeth Hospital, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Geberhiwot+T%22">Geberhiwot T</searchLink>; Endocrinology, Queen Elizabeth Hospital, Birmingham, UK.; University of Birmingham Institute of Metabolism and Systems Research, Birmingham, UK.<br /><searchLink fieldCode="AU" term="%22Steeds+RP%22">Steeds RP</searchLink>; University of Birmingham Institute of Cardiovascular Sciences, Birmingham, UK.; Cardiology, Queen Elizabeth Hospital, Birmingham, UK.
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  Data: <searchLink fieldCode="JN" term="%229602087%22">Heart (British Cardiac Society)</searchLink> [Heart] 2025 Feb 12; Vol. 111 (5), pp. 230-238. <i>Date of Electronic Publication: </i>2025 Feb 12.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22BMJ+Pub%2E+Group%22">BMJ Pub. Group </searchLink><i>Country of Publication: </i>England <i>NLM ID: </i>9602087 <i>Publication Model: </i>Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1468-201X (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2213556037%22">13556037 </searchLink><i>NLM ISO Abbreviation: </i>Heart <i>Subsets: </i>MEDLINE
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        Value: 10.1136/heartjnl-2024-324553
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              Text: 2025 Feb 12
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