Craniosynostosis as a cause of intracranial hypertension in Alagille syndrome: a case series of 6 consecutive pediatric patients.

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Title: Craniosynostosis as a cause of intracranial hypertension in Alagille syndrome: a case series of 6 consecutive pediatric patients.
Authors: Guida L; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.; 2Faculté de Médecine, Université Paris Cité, Paris., Gardin A; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre., James S; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris., Arnaud E; 4Department of Maxillofacial Surgery and Plastic Surgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris., Toujouse C; Departments of5Pediatric Neurology and., Roux J; Departments of5Pediatric Neurology and., Barreau E; 6Ophthalmology, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre, France., Benali Abdallah M; 6Ophthalmology, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre, France., Almes M; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre., Sartori L; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris., Kavoura K; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris., Ackermann O; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre., Gonzales E; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre., Jacquemin E; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre., Khonsari RH; 2Faculté de Médecine, Université Paris Cité, Paris.; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre., Paternoster G; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.
Source: Neurosurgical focus [Neurosurg Focus] 2025 Jan 01; Vol. 58 (1), pp. E6.
Publication Type: Journal Article; Case Reports
Journal Info: Publisher: American Association of Neurological Surgeons Country of Publication: United States NLM ID: 100896471 Publication Model: Print Cited Medium: Internet ISSN: 1092-0684 (Electronic) Linking ISSN: 10920684 NLM ISO Abbreviation: Neurosurg Focus Subsets: MEDLINE
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  Data: Craniosynostosis as a cause of intracranial hypertension in Alagille syndrome: a case series of 6 consecutive pediatric patients.
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  Data: <searchLink fieldCode="AU" term="%22Guida+L%22">Guida L</searchLink>; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.; 2Faculté de Médecine, Université Paris Cité, Paris.<br /><searchLink fieldCode="AU" term="%22Gardin+A%22">Gardin A</searchLink>; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre.<br /><searchLink fieldCode="AU" term="%22James+S%22">James S</searchLink>; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.<br /><searchLink fieldCode="AU" term="%22Arnaud+E%22">Arnaud E</searchLink>; 4Department of Maxillofacial Surgery and Plastic Surgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.<br /><searchLink fieldCode="AU" term="%22Toujouse+C%22">Toujouse C</searchLink>; Departments of5Pediatric Neurology and.<br /><searchLink fieldCode="AU" term="%22Roux+J%22">Roux J</searchLink>; Departments of5Pediatric Neurology and.<br /><searchLink fieldCode="AU" term="%22Barreau+E%22">Barreau E</searchLink>; 6Ophthalmology, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre, France.<br /><searchLink fieldCode="AU" term="%22Benali+Abdallah+M%22">Benali Abdallah M</searchLink>; 6Ophthalmology, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre, France.<br /><searchLink fieldCode="AU" term="%22Almes+M%22">Almes M</searchLink>; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre.<br /><searchLink fieldCode="AU" term="%22Sartori+L%22">Sartori L</searchLink>; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.<br /><searchLink fieldCode="AU" term="%22Kavoura+K%22">Kavoura K</searchLink>; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.<br /><searchLink fieldCode="AU" term="%22Ackermann+O%22">Ackermann O</searchLink>; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre.<br /><searchLink fieldCode="AU" term="%22Gonzales+E%22">Gonzales E</searchLink>; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre.<br /><searchLink fieldCode="AU" term="%22Jacquemin+E%22">Jacquemin E</searchLink>; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre.<br /><searchLink fieldCode="AU" term="%22Khonsari+RH%22">Khonsari RH</searchLink>; 2Faculté de Médecine, Université Paris Cité, Paris.; 3Pediatric Hepatology and Liver Transplantation Unit, National Reference Centre for Biliary Atresia and Genetic Cholestasis, FILFOIE, ERN RARE LIVER, Bicêtre Hospital, Assistance Publique-Hôpitaux de Paris, Paris-Saclay University, Le Kremlin-Bicêtre.<br /><searchLink fieldCode="AU" term="%22Paternoster+G%22">Paternoster G</searchLink>; 1Department of Pediatric Neurosurgery, Hôpital Necker - Enfants Malades, Assistance Publique-Hôpitaux de Paris.
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        Value: 10.3171/2024.10.FOCUS24588
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