A partial deletion of the Tardbp 3'UTR affects TDP-43 regulation and leads to motor dysfunction in mice.

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Title: A partial deletion of the Tardbp 3'UTR affects TDP-43 regulation and leads to motor dysfunction in mice.
Authors: Dinh TTH; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan., Imura C; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan., Shiokawa M; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan., Ayabe S; Experimental Animal Division, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan., Yoshiki A; Experimental Animal Division, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan., Inoue H; iPSC-based Drug Discovery and Development Team, RIKEN BioResource Research Center, 1-7 Hikaridai, Seika-cho, Soraku-gun, Kyoto 619-0237, Japan.; Center for iPS Cell Research and Application (CiRA), Kyoto University, 53 Shogoin Kawahara-cho, Sakyo-ku, Kyoto 606-8507, Japan.; Medical-risk Avoidance based on iPS Cells Team, RIKEN Center for Advanced Intelligence Project (AIP), 53 Shogoin Kawahara, Sakyo, Kyoto 606-8507, Japan., Amano T; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.
Source: Experimental animals [Exp Anim] 2026 Jan 01; Vol. 75 (1), pp. 40-49. Date of Electronic Publication: 2025 Jul 19.
Publication Type: Journal Article
Journal Info: Publisher: Japanese Association for Laboratory Animal Science Country of Publication: Japan NLM ID: 9604830 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1881-7122 (Electronic) Linking ISSN: 00075124 NLM ISO Abbreviation: Exp Anim Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: A partial deletion of the Tardbp 3'UTR affects TDP-43 regulation and leads to motor dysfunction in mice.
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  Data: <searchLink fieldCode="AU" term="%22Dinh+TTH%22">Dinh TTH</searchLink>; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.<br /><searchLink fieldCode="AU" term="%22Imura+C%22">Imura C</searchLink>; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.<br /><searchLink fieldCode="AU" term="%22Shiokawa+M%22">Shiokawa M</searchLink>; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.<br /><searchLink fieldCode="AU" term="%22Ayabe+S%22">Ayabe S</searchLink>; Experimental Animal Division, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.<br /><searchLink fieldCode="AU" term="%22Yoshiki+A%22">Yoshiki A</searchLink>; Experimental Animal Division, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.<br /><searchLink fieldCode="AU" term="%22Inoue+H%22">Inoue H</searchLink>; iPSC-based Drug Discovery and Development Team, RIKEN BioResource Research Center, 1-7 Hikaridai, Seika-cho, Soraku-gun, Kyoto 619-0237, Japan.; Center for iPS Cell Research and Application (CiRA), Kyoto University, 53 Shogoin Kawahara-cho, Sakyo-ku, Kyoto 606-8507, Japan.; Medical-risk Avoidance based on iPS Cells Team, RIKEN Center for Advanced Intelligence Project (AIP), 53 Shogoin Kawahara, Sakyo, Kyoto 606-8507, Japan.<br /><searchLink fieldCode="AU" term="%22Amano+T%22">Amano T</searchLink>; Next Generation Human Disease Model Research Team, RIKEN BioResource Research Center, 3-1-1 Koyadai, Tsukuba, Ibaraki 305-0074, Japan.
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  Data: <searchLink fieldCode="JN" term="%229604830%22">Experimental animals</searchLink> [Exp Anim] 2026 Jan 01; Vol. 75 (1), pp. 40-49. <i>Date of Electronic Publication: </i>2025 Jul 19.
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Japanese+Association+for+Laboratory+Animal+Science%22">Japanese Association for Laboratory Animal Science </searchLink><i>Country of Publication: </i>Japan <i>NLM ID: </i>9604830 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1881-7122 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2200075124%22">00075124 </searchLink><i>NLM ISO Abbreviation: </i>Exp Anim <i>Subsets: </i>MEDLINE
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        Value: 10.1538/expanim.25-0061
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        Text: English
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              Text: 2026 Jan 01
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