Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis.
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| Title: | Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis. |
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| Authors: | Fekrvand S; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Esfahani ZH; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Yarahmadi M; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Saeedi-Boroujeni A; Department of Basic Medical Sciences, Faculty of Medicine, Abadan University of Medical Sciences, Abadan, Iran., Salehi H; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Hakimelahi A; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Almasi-Hashiani A; Department of Epidemiology, School of Health, Arak University of Medical Sciences, Arak, Iran., Rahmati M; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran., Afshar-Ghasemlou S; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran., Fard NNG; Thalassemia & Hemoglobinopathy Research Center, Health Research Institute, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran., Monfared FT; Pediatric Respiratory and Sleep Medicine Research Center, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Afkham EK; Department of Pediatrics, School of Medicine, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Fathi N; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Shad TM; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Babaha F; Department of Pathology and Molecular Medicine, Queen's University, Kingston, ON, Canada., Nazari F; Department of Cellular and Molecular Medicine, Faculty of Medicine, University of Ottawa, 451 Smyth Road, Ottawa, ON K1H 8M5, Canada., Nirouei M; Alborz University of Medical Sciences, Karaj, Iran., Farid AS; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Sanadgol N; Institute of Ophthalmology, University College London, London, UK., Rafiemanesh H; Non-communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran; Department of Epidemiology and Biostatistics, School of Public Health, Alborz University of Medical Sciences, Karaj, Iran., Marzbali MY; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Hassanpour G; Center for Research of Endemic Parasites of Iran, Tehran University of Medical Sciences, Tehran, Iran., Olbrich P; Pediatrics Infectious Diseases, Rheumatology and Immunology Unit, Institute of Biomedicine of Seville, University Hospital Vírgen del Rocío/CSIC/University of Seville, Seville 41013, Spain; Department of Pharmacology, Pediatrics and Radiology, University of Seville, Seville 41008, Spain., Condino-Neto A; Department of Immunology, Institute of Biomedical Sciences, University of São Paulo, 1730 Lineu Prestes Avenue, São Paulo 05508-000, Brazil., Morio T; Department of Pediatrics and Developmental Biology, Tokyo Medical and Dental University (TMDU), Tokyo, Japan., Gennery AR; Translational and Clinical Research Institute, Newcastle University, Newcastle upon Tyne, UK; Paediatric Stem Cell Transplant Unit, Great North Children's Hospital, Newcastle upon Tyne, UK., Meyts I; Inborn Errors of Immunity, Department of Microbiology, Immunology and Transplantation, KU Leuven, Leuven, Belgium; Pediatric Immunodeficiency, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium., Ochs HD; University of Washington School of Medicine, Seattle, WA, USA., Abolhassani H; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran; Division of Immunology, Department of Medical Biochemistry and Biophysics, Karolinska Institute, Stockholm, Sweden., Rezaei N; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Yazdani R; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran. Electronic address: reza_yazdani86@yahoo.com. |
| Source: | Mutation research. Reviews in mutation research [Mutat Res Rev Mutat Res] 2025 Jul-Dec; Vol. 796, pp. 108564. Date of Electronic Publication: 2025 Sep 27. |
| Publication Type: | Journal Article; Systematic Review; Meta-Analysis; Research Support, Non-U.S. Gov't |
| Journal Info: | Publisher: Elsevier Science B.V Country of Publication: Netherlands NLM ID: 101632211 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1388-2139 (Electronic) Linking ISSN: 13835742 NLM ISO Abbreviation: Mutat Res Rev Mutat Res Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 41016093 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Fekrvand+S%22">Fekrvand S</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Esfahani+ZH%22">Esfahani ZH</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Yarahmadi+M%22">Yarahmadi M</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Saeedi-Boroujeni+A%22">Saeedi-Boroujeni A</searchLink>; Department of Basic Medical Sciences, Faculty of Medicine, Abadan University of Medical Sciences, Abadan, Iran.<br /><searchLink fieldCode="AU" term="%22Salehi+H%22">Salehi H</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Hakimelahi+A%22">Hakimelahi A</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Almasi-Hashiani+A%22">Almasi-Hashiani A</searchLink>; Department of Epidemiology, School of Health, Arak University of Medical Sciences, Arak, Iran.<br /><searchLink fieldCode="AU" term="%22Rahmati+M%22">Rahmati M</searchLink>; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.<br /><searchLink fieldCode="AU" term="%22Afshar-Ghasemlou+S%22">Afshar-Ghasemlou S</searchLink>; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.<br /><searchLink fieldCode="AU" term="%22Fard+NNG%22">Fard NNG</searchLink>; Thalassemia & Hemoglobinopathy Research Center, Health Research Institute, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran.<br /><searchLink fieldCode="AU" term="%22Monfared+FT%22">Monfared FT</searchLink>; Pediatric Respiratory and Sleep Medicine Research Center, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Afkham+EK%22">Afkham EK</searchLink>; Department of Pediatrics, School of Medicine, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Fathi+N%22">Fathi N</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Shad+TM%22">Shad TM</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Babaha+F%22">Babaha F</searchLink>; Department of Pathology and Molecular Medicine, Queen's University, Kingston, ON, Canada.<br /><searchLink fieldCode="AU" term="%22Nazari+F%22">Nazari F</searchLink>; Department of Cellular and Molecular Medicine, Faculty of Medicine, University of Ottawa, 451 Smyth Road, Ottawa, ON K1H 8M5, Canada.<br /><searchLink fieldCode="AU" term="%22Nirouei+M%22">Nirouei M</searchLink>; Alborz University of Medical Sciences, Karaj, Iran.<br /><searchLink fieldCode="AU" term="%22Farid+AS%22">Farid AS</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Sanadgol+N%22">Sanadgol N</searchLink>; Institute of Ophthalmology, University College London, London, UK.<br /><searchLink fieldCode="AU" term="%22Rafiemanesh+H%22">Rafiemanesh H</searchLink>; Non-communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran; Department of Epidemiology and Biostatistics, School of Public Health, Alborz University of Medical Sciences, Karaj, Iran.<br /><searchLink fieldCode="AU" term="%22Marzbali+MY%22">Marzbali MY</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Hassanpour+G%22">Hassanpour G</searchLink>; Center for Research of Endemic Parasites of Iran, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Olbrich+P%22">Olbrich P</searchLink>; Pediatrics Infectious Diseases, Rheumatology and Immunology Unit, Institute of Biomedicine of Seville, University Hospital Vírgen del Rocío/CSIC/University of Seville, Seville 41013, Spain; Department of Pharmacology, Pediatrics and Radiology, University of Seville, Seville 41008, Spain.<br /><searchLink fieldCode="AU" term="%22Condino-Neto+A%22">Condino-Neto A</searchLink>; Department of Immunology, Institute of Biomedical Sciences, University of São Paulo, 1730 Lineu Prestes Avenue, São Paulo 05508-000, Brazil.<br /><searchLink fieldCode="AU" term="%22Morio+T%22">Morio T</searchLink>; Department of Pediatrics and Developmental Biology, Tokyo Medical and Dental University (TMDU), Tokyo, Japan.<br /><searchLink fieldCode="AU" term="%22Gennery+AR%22">Gennery AR</searchLink>; Translational and Clinical Research Institute, Newcastle University, Newcastle upon Tyne, UK; Paediatric Stem Cell Transplant Unit, Great North Children's Hospital, Newcastle upon Tyne, UK.<br /><searchLink fieldCode="AU" term="%22Meyts+I%22">Meyts I</searchLink>; Inborn Errors of Immunity, Department of Microbiology, Immunology and Transplantation, KU Leuven, Leuven, Belgium; Pediatric Immunodeficiency, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22Ochs+HD%22">Ochs HD</searchLink>; University of Washington School of Medicine, Seattle, WA, USA.<br /><searchLink fieldCode="AU" term="%22Abolhassani+H%22">Abolhassani H</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran; Division of Immunology, Department of Medical Biochemistry and Biophysics, Karolinska Institute, Stockholm, Sweden.<br /><searchLink fieldCode="AU" term="%22Rezaei+N%22">Rezaei N</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Yazdani+R%22">Yazdani R</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran. Electronic address: reza&#95;yazdani86@yahoo.com. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%22101632211%22">Mutation research. Reviews in mutation research</searchLink> [Mutat Res Rev Mutat Res] 2025 Jul-Dec; Vol. 796, pp. 108564. <i>Date of Electronic Publication: </i>2025 Sep 27. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article; Systematic Review; Meta-Analysis; Research Support, Non-U.S. Gov't – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Elsevier+Science+B%2EV%22">Elsevier Science B.V </searchLink><i>Country of Publication: </i>Netherlands <i>NLM ID: </i>101632211 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1388-2139 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2213835742%22">13835742 </searchLink><i>NLM ISO Abbreviation: </i>Mutat Res Rev Mutat Res <i>Subsets: </i>MEDLINE |
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| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1016/j.mrrev.2025.108564 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 108564 Titles: – TitleFull: Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Fekrvand S – PersonEntity: Name: NameFull: Esfahani ZH – PersonEntity: Name: NameFull: Yarahmadi M – PersonEntity: Name: NameFull: Saeedi-Boroujeni A – PersonEntity: Name: NameFull: Salehi H – PersonEntity: Name: NameFull: Hakimelahi A – PersonEntity: Name: NameFull: Almasi-Hashiani A – PersonEntity: Name: NameFull: Rahmati M – PersonEntity: Name: NameFull: Afshar-Ghasemlou S – PersonEntity: Name: NameFull: Fard NNG – PersonEntity: Name: NameFull: Monfared FT – PersonEntity: Name: NameFull: Afkham EK – PersonEntity: Name: NameFull: Fathi N – PersonEntity: Name: NameFull: Shad TM – PersonEntity: Name: NameFull: Babaha F – PersonEntity: Name: NameFull: Nazari F – PersonEntity: Name: NameFull: Nirouei M – PersonEntity: Name: NameFull: Farid AS – PersonEntity: Name: NameFull: Sanadgol N – PersonEntity: Name: NameFull: Rafiemanesh H – PersonEntity: Name: NameFull: Marzbali MY – PersonEntity: Name: NameFull: Hassanpour G – PersonEntity: Name: NameFull: Olbrich P – PersonEntity: Name: NameFull: Condino-Neto A – PersonEntity: Name: NameFull: Morio T – PersonEntity: Name: NameFull: Gennery AR – PersonEntity: Name: NameFull: Meyts I – PersonEntity: Name: NameFull: Ochs HD – PersonEntity: Name: NameFull: Abolhassani H – PersonEntity: Name: NameFull: Rezaei N – PersonEntity: Name: NameFull: Yazdani R IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 07 Text: 2025 Jul-Dec Type: published Y: 2025 Identifiers: – Type: issn-electronic Value: 1388-2139 Numbering: – Type: volume Value: 796 Titles: – TitleFull: Mutation research. Reviews in mutation research Type: main |
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