Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis.

Saved in:
Bibliographic Details
Title: Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis.
Authors: Fekrvand S; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Esfahani ZH; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Yarahmadi M; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Saeedi-Boroujeni A; Department of Basic Medical Sciences, Faculty of Medicine, Abadan University of Medical Sciences, Abadan, Iran., Salehi H; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Hakimelahi A; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Almasi-Hashiani A; Department of Epidemiology, School of Health, Arak University of Medical Sciences, Arak, Iran., Rahmati M; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran., Afshar-Ghasemlou S; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran., Fard NNG; Thalassemia & Hemoglobinopathy Research Center, Health Research Institute, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran., Monfared FT; Pediatric Respiratory and Sleep Medicine Research Center, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Afkham EK; Department of Pediatrics, School of Medicine, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Fathi N; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Shad TM; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Babaha F; Department of Pathology and Molecular Medicine, Queen's University, Kingston, ON, Canada., Nazari F; Department of Cellular and Molecular Medicine, Faculty of Medicine, University of Ottawa, 451 Smyth Road, Ottawa, ON K1H 8M5, Canada., Nirouei M; Alborz University of Medical Sciences, Karaj, Iran., Farid AS; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran., Sanadgol N; Institute of Ophthalmology, University College London, London, UK., Rafiemanesh H; Non-communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran; Department of Epidemiology and Biostatistics, School of Public Health, Alborz University of Medical Sciences, Karaj, Iran., Marzbali MY; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Hassanpour G; Center for Research of Endemic Parasites of Iran, Tehran University of Medical Sciences, Tehran, Iran., Olbrich P; Pediatrics Infectious Diseases, Rheumatology and Immunology Unit, Institute of Biomedicine of Seville, University Hospital Vírgen del Rocío/CSIC/University of Seville, Seville 41013, Spain; Department of Pharmacology, Pediatrics and Radiology, University of Seville, Seville 41008, Spain., Condino-Neto A; Department of Immunology, Institute of Biomedical Sciences, University of São Paulo, 1730 Lineu Prestes Avenue, São Paulo 05508-000, Brazil., Morio T; Department of Pediatrics and Developmental Biology, Tokyo Medical and Dental University (TMDU), Tokyo, Japan., Gennery AR; Translational and Clinical Research Institute, Newcastle University, Newcastle upon Tyne, UK; Paediatric Stem Cell Transplant Unit, Great North Children's Hospital, Newcastle upon Tyne, UK., Meyts I; Inborn Errors of Immunity, Department of Microbiology, Immunology and Transplantation, KU Leuven, Leuven, Belgium; Pediatric Immunodeficiency, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium., Ochs HD; University of Washington School of Medicine, Seattle, WA, USA., Abolhassani H; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran; Division of Immunology, Department of Medical Biochemistry and Biophysics, Karolinska Institute, Stockholm, Sweden., Rezaei N; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran., Yazdani R; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran. Electronic address: reza_yazdani86@yahoo.com.
Source: Mutation research. Reviews in mutation research [Mutat Res Rev Mutat Res] 2025 Jul-Dec; Vol. 796, pp. 108564. Date of Electronic Publication: 2025 Sep 27.
Publication Type: Journal Article; Systematic Review; Meta-Analysis; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Elsevier Science B.V Country of Publication: Netherlands NLM ID: 101632211 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1388-2139 (Electronic) Linking ISSN: 13835742 NLM ISO Abbreviation: Mutat Res Rev Mutat Res Subsets: MEDLINE
Database: MEDLINE Ultimate
FullText Text:
  Availability: 0
Header DbId: mdl
DbLabel: MEDLINE Ultimate
An: 41016093
AccessLevel: 2
PubType: Academic Journal
PubTypeId: academicJournal
PreciseRelevancyScore: 0
IllustrationInfo
Items – Name: Title
  Label: Title
  Group: Ti
  Data: Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis.
– Name: Author
  Label: Authors
  Group: Au
  Data: <searchLink fieldCode="AU" term="%22Fekrvand+S%22">Fekrvand S</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Esfahani+ZH%22">Esfahani ZH</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Yarahmadi+M%22">Yarahmadi M</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Saeedi-Boroujeni+A%22">Saeedi-Boroujeni A</searchLink>; Department of Basic Medical Sciences, Faculty of Medicine, Abadan University of Medical Sciences, Abadan, Iran.<br /><searchLink fieldCode="AU" term="%22Salehi+H%22">Salehi H</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Hakimelahi+A%22">Hakimelahi A</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Almasi-Hashiani+A%22">Almasi-Hashiani A</searchLink>; Department of Epidemiology, School of Health, Arak University of Medical Sciences, Arak, Iran.<br /><searchLink fieldCode="AU" term="%22Rahmati+M%22">Rahmati M</searchLink>; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.<br /><searchLink fieldCode="AU" term="%22Afshar-Ghasemlou+S%22">Afshar-Ghasemlou S</searchLink>; Department of Immunology, Faculty of Medicine, Isfahan University of Medical Sciences, Isfahan, Iran.<br /><searchLink fieldCode="AU" term="%22Fard+NNG%22">Fard NNG</searchLink>; Thalassemia & Hemoglobinopathy Research Center, Health Research Institute, Ahvaz Jundishapur University of Medical Sciences, Ahvaz, Iran.<br /><searchLink fieldCode="AU" term="%22Monfared+FT%22">Monfared FT</searchLink>; Pediatric Respiratory and Sleep Medicine Research Center, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Afkham+EK%22">Afkham EK</searchLink>; Department of Pediatrics, School of Medicine, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Fathi+N%22">Fathi N</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Shad+TM%22">Shad TM</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Babaha+F%22">Babaha F</searchLink>; Department of Pathology and Molecular Medicine, Queen's University, Kingston, ON, Canada.<br /><searchLink fieldCode="AU" term="%22Nazari+F%22">Nazari F</searchLink>; Department of Cellular and Molecular Medicine, Faculty of Medicine, University of Ottawa, 451 Smyth Road, Ottawa, ON K1H 8M5, Canada.<br /><searchLink fieldCode="AU" term="%22Nirouei+M%22">Nirouei M</searchLink>; Alborz University of Medical Sciences, Karaj, Iran.<br /><searchLink fieldCode="AU" term="%22Farid+AS%22">Farid AS</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Sanadgol+N%22">Sanadgol N</searchLink>; Institute of Ophthalmology, University College London, London, UK.<br /><searchLink fieldCode="AU" term="%22Rafiemanesh+H%22">Rafiemanesh H</searchLink>; Non-communicable Diseases Research Center, Alborz University of Medical Sciences, Karaj, Iran; Department of Epidemiology and Biostatistics, School of Public Health, Alborz University of Medical Sciences, Karaj, Iran.<br /><searchLink fieldCode="AU" term="%22Marzbali+MY%22">Marzbali MY</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Hassanpour+G%22">Hassanpour G</searchLink>; Center for Research of Endemic Parasites of Iran, Tehran University of Medical Sciences, Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Olbrich+P%22">Olbrich P</searchLink>; Pediatrics Infectious Diseases, Rheumatology and Immunology Unit, Institute of Biomedicine of Seville, University Hospital Vírgen del Rocío/CSIC/University of Seville, Seville 41013, Spain; Department of Pharmacology, Pediatrics and Radiology, University of Seville, Seville 41008, Spain.<br /><searchLink fieldCode="AU" term="%22Condino-Neto+A%22">Condino-Neto A</searchLink>; Department of Immunology, Institute of Biomedical Sciences, University of São Paulo, 1730 Lineu Prestes Avenue, São Paulo 05508-000, Brazil.<br /><searchLink fieldCode="AU" term="%22Morio+T%22">Morio T</searchLink>; Department of Pediatrics and Developmental Biology, Tokyo Medical and Dental University (TMDU), Tokyo, Japan.<br /><searchLink fieldCode="AU" term="%22Gennery+AR%22">Gennery AR</searchLink>; Translational and Clinical Research Institute, Newcastle University, Newcastle upon Tyne, UK; Paediatric Stem Cell Transplant Unit, Great North Children's Hospital, Newcastle upon Tyne, UK.<br /><searchLink fieldCode="AU" term="%22Meyts+I%22">Meyts I</searchLink>; Inborn Errors of Immunity, Department of Microbiology, Immunology and Transplantation, KU Leuven, Leuven, Belgium; Pediatric Immunodeficiency, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium.<br /><searchLink fieldCode="AU" term="%22Ochs+HD%22">Ochs HD</searchLink>; University of Washington School of Medicine, Seattle, WA, USA.<br /><searchLink fieldCode="AU" term="%22Abolhassani+H%22">Abolhassani H</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran; Division of Immunology, Department of Medical Biochemistry and Biophysics, Karolinska Institute, Stockholm, Sweden.<br /><searchLink fieldCode="AU" term="%22Rezaei+N%22">Rezaei N</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran.<br /><searchLink fieldCode="AU" term="%22Yazdani+R%22">Yazdani R</searchLink>; Research Center for Immunodeficiencies, Pediatrics Center of Excellence, Children's Medical Center, Tehran University of Medical Sciences, Tehran, Iran; Primary Immunodeficiency Diseases Network (PIDNet), Universal Scientific Education and Research Network (USERN), Tehran, Iran. Electronic address: reza_yazdani86@yahoo.com.
– Name: TitleSource
  Label: Source
  Group: Src
  Data: <searchLink fieldCode="JN" term="%22101632211%22">Mutation research. Reviews in mutation research</searchLink> [Mutat Res Rev Mutat Res] 2025 Jul-Dec; Vol. 796, pp. 108564. <i>Date of Electronic Publication: </i>2025 Sep 27.
– Name: TypePub
  Label: Publication Type
  Group: TypPub
  Data: Journal Article; Systematic Review; Meta-Analysis; Research Support, Non-U.S. Gov't
– Name: TitleSource
  Label: Journal Info
  Group: Src
  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Elsevier+Science+B%2EV%22">Elsevier Science B.V </searchLink><i>Country of Publication: </i>Netherlands <i>NLM ID: </i>101632211 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1388-2139 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2213835742%22">13835742 </searchLink><i>NLM ISO Abbreviation: </i>Mutat Res Rev Mutat Res <i>Subsets: </i>MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41016093
RecordInfo BibRecord:
  BibEntity:
    Identifiers:
      – Type: doi
        Value: 10.1016/j.mrrev.2025.108564
    Languages:
      – Code: eng
        Text: English
    PhysicalDescription:
      Pagination:
        StartPage: 108564
    Titles:
      – TitleFull: Mortality rate and causes of death in inborn errors of immunity: A systematic review and meta-analysis.
        Type: main
  BibRelationships:
    HasContributorRelationships:
      – PersonEntity:
          Name:
            NameFull: Fekrvand S
      – PersonEntity:
          Name:
            NameFull: Esfahani ZH
      – PersonEntity:
          Name:
            NameFull: Yarahmadi M
      – PersonEntity:
          Name:
            NameFull: Saeedi-Boroujeni A
      – PersonEntity:
          Name:
            NameFull: Salehi H
      – PersonEntity:
          Name:
            NameFull: Hakimelahi A
      – PersonEntity:
          Name:
            NameFull: Almasi-Hashiani A
      – PersonEntity:
          Name:
            NameFull: Rahmati M
      – PersonEntity:
          Name:
            NameFull: Afshar-Ghasemlou S
      – PersonEntity:
          Name:
            NameFull: Fard NNG
      – PersonEntity:
          Name:
            NameFull: Monfared FT
      – PersonEntity:
          Name:
            NameFull: Afkham EK
      – PersonEntity:
          Name:
            NameFull: Fathi N
      – PersonEntity:
          Name:
            NameFull: Shad TM
      – PersonEntity:
          Name:
            NameFull: Babaha F
      – PersonEntity:
          Name:
            NameFull: Nazari F
      – PersonEntity:
          Name:
            NameFull: Nirouei M
      – PersonEntity:
          Name:
            NameFull: Farid AS
      – PersonEntity:
          Name:
            NameFull: Sanadgol N
      – PersonEntity:
          Name:
            NameFull: Rafiemanesh H
      – PersonEntity:
          Name:
            NameFull: Marzbali MY
      – PersonEntity:
          Name:
            NameFull: Hassanpour G
      – PersonEntity:
          Name:
            NameFull: Olbrich P
      – PersonEntity:
          Name:
            NameFull: Condino-Neto A
      – PersonEntity:
          Name:
            NameFull: Morio T
      – PersonEntity:
          Name:
            NameFull: Gennery AR
      – PersonEntity:
          Name:
            NameFull: Meyts I
      – PersonEntity:
          Name:
            NameFull: Ochs HD
      – PersonEntity:
          Name:
            NameFull: Abolhassani H
      – PersonEntity:
          Name:
            NameFull: Rezaei N
      – PersonEntity:
          Name:
            NameFull: Yazdani R
    IsPartOfRelationships:
      – BibEntity:
          Dates:
            – D: 01
              M: 07
              Text: 2025 Jul-Dec
              Type: published
              Y: 2025
          Identifiers:
            – Type: issn-electronic
              Value: 1388-2139
          Numbering:
            – Type: volume
              Value: 796
          Titles:
            – TitleFull: Mutation research. Reviews in mutation research
              Type: main
ResultId 1