Paediatric pulmonary arterial hypertension following congenital heart defect repair: enhanced risk stratification and outcomes in a national cohort.

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Title: Paediatric pulmonary arterial hypertension following congenital heart defect repair: enhanced risk stratification and outcomes in a national cohort.
Authors: Constantine A; National Paediatric Pulmonary Hypertension Service UK, Great Ormond Street Hospital for Children NHS Foundation Trust, Great Ormond Street, London WC1N 3JH, UK.; Adult Congenital Heart Disease Unit, Queen Elizabeth Hospital Birmingham, University Hospitals Birmingham NHS Foundation Trust, Birmingham B15 2GW, UK.; Department of Cardiovascular Sciences, University of Birmingham, Birmingham B15 2TT, UK., Dimopoulos K; Adult Congenital Heart Centre and National Centre for Pulmonary Hypertension, Royal Brompton Hospital, Royal Brompton & Harefield NHS Foundation Trust, London SW3 6NP, UK.; National Heart and Lung Institute, Imperial College London, London SW3 6LY, UK., Condliffe R; Pulmonary Vascular Disease Unit, Royal Hallamshire Hospital, Sheffield S10 2JF, UK., Clift P; Adult Congenital Heart Disease Unit, Queen Elizabeth Hospital Birmingham, University Hospitals Birmingham NHS Foundation Trust, Birmingham B15 2GW, UK.; Department of Cardiovascular Sciences, University of Birmingham, Birmingham B15 2TT, UK., Jansen K; Adult Congenital and Paediatric Heart Unit, Freeman Hospital Newcastle Upon Tyne Hospitals NHS Foundation Trust, Newcastle Upon Tyne NE7 7DN, UK.; Population Health Sciences Institute, Newcastle University, Newcastle upon Tyne NE2 4AX, UK., Wort SJ; Adult Congenital Heart Centre and National Centre for Pulmonary Hypertension, Royal Brompton Hospital, Royal Brompton & Harefield NHS Foundation Trust, London SW3 6NP, UK.; National Heart and Lung Institute, Imperial College London, London SW3 6LY, UK., Chaplin G; UCL Institute of Cardiovascular Science, University College London, Gower Street, London WC1E 6BT, UK., Krishnathasan K; Adult Congenital Heart Disease Unit, Queen Elizabeth Hospital Birmingham, University Hospitals Birmingham NHS Foundation Trust, Birmingham B15 2GW, UK.; Department of Cardiovascular Sciences, University of Birmingham, Birmingham B15 2TT, UK., Dhillon R; Birmingham Children's Hospital, Birmingham Women's and Children's NHS Foundation Trust, Birmingham B4 6NH, UK., Mookerjee J; Royal Manchester Children's Hospital, Manchester University NHS Foundation Trust, Manchester M13 9WL, UK., Knight WB; Royal Hospital for Children, NHS Greater Glasgow and Clyde, Glasgow G51 4TF, Scotland., Jones CB; Alder Hey Children's Hospital, Alder Hey Children's NHS Foundation Trust, Liverpool L12 2AP, UK., Forte MNV; Bristol Royal Hospital for Children, University Hospitals Bristol and Weston NHS Foundation Trust, Bristol BS2 8BJ, UK., Wilson D; Department of Paediatric Cardiology, University Hospital of Wales, Cardiff CF14 4XW, UK., Michael H; Leeds General Infirmary, The Leeds Teaching Hospitals NHS Trust, Leeds LS1 3EX, UK., Mendoza Soto A; Pediatric Heart Institute, University Hospital 12 de Octubre, Madrid 28041, Spain.; Instituto de Investigación Sanitaria Hospital 12 de Octubre, Madrid 28041, Spain., Labrandero C; Servicio de Cardiología Infantil, Hospital Universitario La Paz, Madrid 28046, Spain., Rodríguez Ogando A; Unidad de Cardiopatías Congénitas (UCC), Servicio de Cardiología Infantil, Hospital Universitario Gregorio Marañón, Madrid 28007, Spain., Moreno-Galdó A; Paediatric Pulmonology Section, Department of Paediatrics, Hospital Universitario Vall d´Hebron, Barcelona 08035, Spain., Guillén Rodríguez I; Sección de Cardiología y Hemodinámica Infantil, Hospital Universitario Virgen del Rocío, Seville 41013, Spain., Cuenca LMC; Department of Paediatric Cardiology, Clínica Shaio, Bogotá 111121, Colombia., Perin F; Unidad de Cardiología Pediátrica, Hospital Universitario Virgen de las Nieves, Granada 18014, Spain., Bonora AM; Unidad de Cardiología Pediátrica, Hospital Universitario y Politécnico La Fe, Valencia 46026, Spain., López Ramón M; Servicio de Cardiología Pediátrica, Hospital Universitario Miguel Servet, Zaragoza 50009, Spain., Albert SV; Unidad de Cardiopatías Congénitas (UCC), Hospital Universitario Ramón y Cajal, Madrid 28002, Spain., Riezu MÁI; Sección de Cardiología Pediátrica, Hospital Universitario Donostia, San Sebastián (Guipúzcoa) 20014, País Vasco, Spain., Espín López JM; Sección de Cardiología Pediátrica, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia 30120, Spain., Del Cerro Marín MJ; Servicio de Cardiología infantil, Hospital Universitario Ramón y Cajal, Madrid, Spain., Moledina S; National Paediatric Pulmonary Hypertension Service UK, Great Ormond Street Hospital for Children NHS Foundation Trust, Great Ormond Street, London WC1N 3JH, UK.; UCL Institute of Cardiovascular Science, University College London, Gower Street, London WC1E 6BT, UK.
Source: European heart journal. Quality of care & clinical outcomes [Eur Heart J Qual Care Clin Outcomes] 2026 Apr 29; Vol. 12 (3), pp. 325-335.
Publication Type: Journal Article; Multicenter Study
Journal Info: Publisher: Oxford University Press Country of Publication: England NLM ID: 101677796 Publication Model: Print Cited Medium: Internet ISSN: 2058-1742 (Electronic) Linking ISSN: 20581742 NLM ISO Abbreviation: Eur Heart J Qual Care Clin Outcomes Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Paediatric pulmonary arterial hypertension following congenital heart defect repair: enhanced risk stratification and outcomes in a national cohort.
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  Data: <searchLink fieldCode="AU" term="%22Constantine+A%22">Constantine A</searchLink>; National Paediatric Pulmonary Hypertension Service UK, Great Ormond Street Hospital for Children NHS Foundation Trust, Great Ormond Street, London WC1N 3JH, UK.; Adult Congenital Heart Disease Unit, Queen Elizabeth Hospital Birmingham, University Hospitals Birmingham NHS Foundation Trust, Birmingham B15 2GW, UK.; Department of Cardiovascular Sciences, University of Birmingham, Birmingham B15 2TT, UK.<br /><searchLink fieldCode="AU" term="%22Dimopoulos+K%22">Dimopoulos K</searchLink>; Adult Congenital Heart Centre and National Centre for Pulmonary Hypertension, Royal Brompton Hospital, Royal Brompton & Harefield NHS Foundation Trust, London SW3 6NP, UK.; National Heart and Lung Institute, Imperial College London, London SW3 6LY, UK.<br /><searchLink fieldCode="AU" term="%22Condliffe+R%22">Condliffe R</searchLink>; Pulmonary Vascular Disease Unit, Royal Hallamshire Hospital, Sheffield S10 2JF, UK.<br /><searchLink fieldCode="AU" term="%22Clift+P%22">Clift P</searchLink>; Adult Congenital Heart Disease Unit, Queen Elizabeth Hospital Birmingham, University Hospitals Birmingham NHS Foundation Trust, Birmingham B15 2GW, UK.; Department of Cardiovascular Sciences, University of Birmingham, Birmingham B15 2TT, UK.<br /><searchLink fieldCode="AU" term="%22Jansen+K%22">Jansen K</searchLink>; Adult Congenital and Paediatric Heart Unit, Freeman Hospital Newcastle Upon Tyne Hospitals NHS Foundation Trust, Newcastle Upon Tyne NE7 7DN, UK.; Population Health Sciences Institute, Newcastle University, Newcastle upon Tyne NE2 4AX, UK.<br /><searchLink fieldCode="AU" term="%22Wort+SJ%22">Wort SJ</searchLink>; Adult Congenital Heart Centre and National Centre for Pulmonary Hypertension, Royal Brompton Hospital, Royal Brompton & Harefield NHS Foundation Trust, London SW3 6NP, UK.; National Heart and Lung Institute, Imperial College London, London SW3 6LY, UK.<br /><searchLink fieldCode="AU" term="%22Chaplin+G%22">Chaplin G</searchLink>; UCL Institute of Cardiovascular Science, University College London, Gower Street, London WC1E 6BT, UK.<br /><searchLink fieldCode="AU" term="%22Krishnathasan+K%22">Krishnathasan K</searchLink>; Adult Congenital Heart Disease Unit, Queen Elizabeth Hospital Birmingham, University Hospitals Birmingham NHS Foundation Trust, Birmingham B15 2GW, UK.; Department of Cardiovascular Sciences, University of Birmingham, Birmingham B15 2TT, UK.<br /><searchLink fieldCode="AU" term="%22Dhillon+R%22">Dhillon R</searchLink>; Birmingham Children's Hospital, Birmingham Women's and Children's NHS Foundation Trust, Birmingham B4 6NH, UK.<br /><searchLink fieldCode="AU" term="%22Mookerjee+J%22">Mookerjee J</searchLink>; Royal Manchester Children's Hospital, Manchester University NHS Foundation Trust, Manchester M13 9WL, UK.<br /><searchLink fieldCode="AU" term="%22Knight+WB%22">Knight WB</searchLink>; Royal Hospital for Children, NHS Greater Glasgow and Clyde, Glasgow G51 4TF, Scotland.<br /><searchLink fieldCode="AU" term="%22Jones+CB%22">Jones CB</searchLink>; Alder Hey Children's Hospital, Alder Hey Children's NHS Foundation Trust, Liverpool L12 2AP, UK.<br /><searchLink fieldCode="AU" term="%22Forte+MNV%22">Forte MNV</searchLink>; Bristol Royal Hospital for Children, University Hospitals Bristol and Weston NHS Foundation Trust, Bristol BS2 8BJ, UK.<br /><searchLink fieldCode="AU" term="%22Wilson+D%22">Wilson D</searchLink>; Department of Paediatric Cardiology, University Hospital of Wales, Cardiff CF14 4XW, UK.<br /><searchLink fieldCode="AU" term="%22Michael+H%22">Michael H</searchLink>; Leeds General Infirmary, The Leeds Teaching Hospitals NHS Trust, Leeds LS1 3EX, UK.<br /><searchLink fieldCode="AU" term="%22Mendoza+Soto+A%22">Mendoza Soto A</searchLink>; Pediatric Heart Institute, University Hospital 12 de Octubre, Madrid 28041, Spain.; Instituto de Investigación Sanitaria Hospital 12 de Octubre, Madrid 28041, Spain.<br /><searchLink fieldCode="AU" term="%22Labrandero+C%22">Labrandero C</searchLink>; Servicio de Cardiología Infantil, Hospital Universitario La Paz, Madrid 28046, Spain.<br /><searchLink fieldCode="AU" term="%22Rodríguez+Ogando+A%22">Rodríguez Ogando A</searchLink>; Unidad de Cardiopatías Congénitas (UCC), Servicio de Cardiología Infantil, Hospital Universitario Gregorio Marañón, Madrid 28007, Spain.<br /><searchLink fieldCode="AU" term="%22Moreno-Galdó+A%22">Moreno-Galdó A</searchLink>; Paediatric Pulmonology Section, Department of Paediatrics, Hospital Universitario Vall d´Hebron, Barcelona 08035, Spain.<br /><searchLink fieldCode="AU" term="%22Guillén+Rodríguez+I%22">Guillén Rodríguez I</searchLink>; Sección de Cardiología y Hemodinámica Infantil, Hospital Universitario Virgen del Rocío, Seville 41013, Spain.<br /><searchLink fieldCode="AU" term="%22Cuenca+LMC%22">Cuenca LMC</searchLink>; Department of Paediatric Cardiology, Clínica Shaio, Bogotá 111121, Colombia.<br /><searchLink fieldCode="AU" term="%22Perin+F%22">Perin F</searchLink>; Unidad de Cardiología Pediátrica, Hospital Universitario Virgen de las Nieves, Granada 18014, Spain.<br /><searchLink fieldCode="AU" term="%22Bonora+AM%22">Bonora AM</searchLink>; Unidad de Cardiología Pediátrica, Hospital Universitario y Politécnico La Fe, Valencia 46026, Spain.<br /><searchLink fieldCode="AU" term="%22López+Ramón+M%22">López Ramón M</searchLink>; Servicio de Cardiología Pediátrica, Hospital Universitario Miguel Servet, Zaragoza 50009, Spain.<br /><searchLink fieldCode="AU" term="%22Albert+SV%22">Albert SV</searchLink>; Unidad de Cardiopatías Congénitas (UCC), Hospital Universitario Ramón y Cajal, Madrid 28002, Spain.<br /><searchLink fieldCode="AU" term="%22Riezu+MÁI%22">Riezu MÁI</searchLink>; Sección de Cardiología Pediátrica, Hospital Universitario Donostia, San Sebastián (Guipúzcoa) 20014, País Vasco, Spain.<br /><searchLink fieldCode="AU" term="%22Espín+López+JM%22">Espín López JM</searchLink>; Sección de Cardiología Pediátrica, Hospital Clínico Universitario Virgen de la Arrixaca, Murcia 30120, Spain.<br /><searchLink fieldCode="AU" term="%22Del+Cerro+Marín+MJ%22">Del Cerro Marín MJ</searchLink>; Servicio de Cardiología infantil, Hospital Universitario Ramón y Cajal, Madrid, Spain.<br /><searchLink fieldCode="AU" term="%22Moledina+S%22">Moledina S</searchLink>; National Paediatric Pulmonary Hypertension Service UK, Great Ormond Street Hospital for Children NHS Foundation Trust, Great Ormond Street, London WC1N 3JH, UK.; UCL Institute of Cardiovascular Science, University College London, Gower Street, London WC1E 6BT, UK.
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