Systemic Disease Progression and Neurodegeneration in the Gbe1ys/ys Mouse Model of Glycogen Storage Disease Type IV.
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| Title: | Systemic Disease Progression and Neurodegeneration in the Gbe1ys/ys Mouse Model of Glycogen Storage Disease Type IV. |
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| Authors: | Choi SJ; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Koch RL; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Gibson RA; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Weaver FE; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Adhikari Y; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Eisner W; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Mehta A; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Jeck WR; Department of Pathology, Duke University Medical Center, Durham, North Carolina., Lim JA; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: jeonga.lim@duke.edu., Kishnani PS; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: priya.kishnani@duke.edu. |
| Source: | The American journal of pathology [Am J Pathol] 2026 Mar; Vol. 196 (3), pp. 731-744. Date of Electronic Publication: 2025 Dec 15. |
| Publication Type: | Journal Article |
| Journal Info: | Publisher: Elsevier Country of Publication: United States NLM ID: 0370502 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1525-2191 (Electronic) Linking ISSN: 00029440 NLM ISO Abbreviation: Am J Pathol Subsets: MEDLINE |
| Database: | MEDLINE Ultimate |
| FullText | Text: Availability: 0 |
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| Header | DbId: mdl DbLabel: MEDLINE Ultimate An: 41407198 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| Items | – Name: Title Label: Title Group: Ti Data: Systemic Disease Progression and Neurodegeneration in the Gbe1<superscript>ys/ys</superscript> Mouse Model of Glycogen Storage Disease Type IV. – Name: Author Label: Authors Group: Au Data: <searchLink fieldCode="AU" term="%22Choi+SJ%22">Choi SJ</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Koch+RL%22">Koch RL</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Gibson+RA%22">Gibson RA</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Weaver+FE%22">Weaver FE</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Adhikari+Y%22">Adhikari Y</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Eisner+W%22">Eisner W</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Mehta+A%22">Mehta A</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Jeck+WR%22">Jeck WR</searchLink>; Department of Pathology, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Lim+JA%22">Lim JA</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: jeonga.lim@duke.edu.<br /><searchLink fieldCode="AU" term="%22Kishnani+PS%22">Kishnani PS</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: priya.kishnani@duke.edu. – Name: TitleSource Label: Source Group: Src Data: <searchLink fieldCode="JN" term="%220370502%22">The American journal of pathology</searchLink> [Am J Pathol] 2026 Mar; Vol. 196 (3), pp. 731-744. <i>Date of Electronic Publication: </i>2025 Dec 15. – Name: TypePub Label: Publication Type Group: TypPub Data: Journal Article – Name: TitleSource Label: Journal Info Group: Src Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Elsevier%22">Elsevier </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>0370502 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1525-2191 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2200029440%22">00029440 </searchLink><i>NLM ISO Abbreviation: </i>Am J Pathol <i>Subsets: </i>MEDLINE |
| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=41407198 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1016/j.ajpath.2025.11.006 Languages: – Code: eng Text: English PhysicalDescription: Pagination: StartPage: 731 Titles: – TitleFull: Systemic Disease Progression and Neurodegeneration in the Gbe1ys/ys Mouse Model of Glycogen Storage Disease Type IV. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Choi SJ – PersonEntity: Name: NameFull: Koch RL – PersonEntity: Name: NameFull: Gibson RA – PersonEntity: Name: NameFull: Weaver FE – PersonEntity: Name: NameFull: Adhikari Y – PersonEntity: Name: NameFull: Eisner W – PersonEntity: Name: NameFull: Mehta A – PersonEntity: Name: NameFull: Jeck WR – PersonEntity: Name: NameFull: Lim JA – PersonEntity: Name: NameFull: Kishnani PS IsPartOfRelationships: – BibEntity: Dates: – D: 01 M: 03 Text: 2026 Mar Type: published Y: 2026 Identifiers: – Type: issn-electronic Value: 1525-2191 Numbering: – Type: volume Value: 196 – Type: issue Value: 3 Titles: – TitleFull: The American journal of pathology Type: main |
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