Systemic Disease Progression and Neurodegeneration in the Gbe1ys/ys Mouse Model of Glycogen Storage Disease Type IV.

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Title: Systemic Disease Progression and Neurodegeneration in the Gbe1ys/ys Mouse Model of Glycogen Storage Disease Type IV.
Authors: Choi SJ; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Koch RL; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Gibson RA; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Weaver FE; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Adhikari Y; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Eisner W; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Mehta A; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina., Jeck WR; Department of Pathology, Duke University Medical Center, Durham, North Carolina., Lim JA; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: jeonga.lim@duke.edu., Kishnani PS; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: priya.kishnani@duke.edu.
Source: The American journal of pathology [Am J Pathol] 2026 Mar; Vol. 196 (3), pp. 731-744. Date of Electronic Publication: 2025 Dec 15.
Publication Type: Journal Article
Journal Info: Publisher: Elsevier Country of Publication: United States NLM ID: 0370502 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1525-2191 (Electronic) Linking ISSN: 00029440 NLM ISO Abbreviation: Am J Pathol Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Systemic Disease Progression and Neurodegeneration in the Gbe1<superscript>ys/ys</superscript> Mouse Model of Glycogen Storage Disease Type IV.
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  Data: <searchLink fieldCode="AU" term="%22Choi+SJ%22">Choi SJ</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Koch+RL%22">Koch RL</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Gibson+RA%22">Gibson RA</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Weaver+FE%22">Weaver FE</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Adhikari+Y%22">Adhikari Y</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Eisner+W%22">Eisner W</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Mehta+A%22">Mehta A</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Jeck+WR%22">Jeck WR</searchLink>; Department of Pathology, Duke University Medical Center, Durham, North Carolina.<br /><searchLink fieldCode="AU" term="%22Lim+JA%22">Lim JA</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: jeonga.lim@duke.edu.<br /><searchLink fieldCode="AU" term="%22Kishnani+PS%22">Kishnani PS</searchLink>; Division of Medical Genetics, Department of Pediatrics, Duke University Medical Center, Durham, North Carolina. Electronic address: priya.kishnani@duke.edu.
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        Value: 10.1016/j.ajpath.2025.11.006
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              Text: 2026 Mar
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