Asymmetrical muscular disorder with normal creatine kinase (CK) and electromyography (EMG): the challenging diagnosis of muscular polyarteritis nodosa (MPAN), case report and literature review.

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Title: Asymmetrical muscular disorder with normal creatine kinase (CK) and electromyography (EMG): the challenging diagnosis of muscular polyarteritis nodosa (MPAN), case report and literature review.
Authors: Dib A; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France. alexandre.dib@chu-lyon.fr.; Service ENMG Et de Pathologies Neuromusculaires, Centre de Référence Des Maladies Neuromusculaires PACA-Réunion-Rhône Alpes, Hôpital Neurologique P. Wertheimer, Hospices Civils de Lyon, Bron, France. alexandre.dib@chu-lyon.fr., Lequain H; Department of Internal Medicine, Centre de Référence Des Maladies Auto-Inflammatoires Et de L'Amylose Inflammatoire (CéRéMAIA), Hôpital de La Croix-Rousse, Hospices Civils de Lyon, Université Claude-Bernard Lyon 1, Lyon, France., Fenouil T; Institute of Pathology - East Site, Groupement Hospitalier Est, Hospices Civils de Lyon, Bron, France., Pegat A; Service ENMG Et de Pathologies Neuromusculaires, Centre de Référence Des Maladies Neuromusculaires PACA-Réunion-Rhône Alpes, Hôpital Neurologique P. Wertheimer, Hospices Civils de Lyon, Bron, France., Petiot P; Service ENMG Et de Pathologies Neuromusculaires, Centre de Référence Des Maladies Neuromusculaires PACA-Réunion-Rhône Alpes, Hôpital Neurologique P. Wertheimer, Hospices Civils de Lyon, Bron, France., Barta A; Department of Diagnostic and Interventional Radiology, Hôpital Edouard Herriot, Hospices Civils de Lyon, Lyon, France., Mayard C; Department of Diagnostic and Interventional Radiology, Hôpital Edouard Herriot, Hospices Civils de Lyon, Lyon, France., Balletti A; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France., Virot E; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.; Constitutive Reference Center, Major Sickle Cell Syndromes, Thalassemia and Other Rare Pathologies of Red Blood Cell and Erythropoiesis, Edouard Herriot Hospital, Lyon, France., Pascu I; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France., Hot A; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.; Constitutive Reference Center, Major Sickle Cell Syndromes, Thalassemia and Other Rare Pathologies of Red Blood Cell and Erythropoiesis, Edouard Herriot Hospital, Lyon, France., Gallay L; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.; Institut NeuroMyoGène, Laboratoire Physiopathologie Et Génétique du Neurone Et du Muscle, CNRS UMR 5261 - Inserm U1315, Université Claude Bernard Lyon 1, Lyon, France.
Source: Neurological sciences : official journal of the Italian Neurological Society and of the Italian Society of Clinical Neurophysiology [Neurol Sci] 2026 Jun 29; Vol. 47 (7). Date of Electronic Publication: 2026 Jun 29.
Publication Type: Case Reports; Journal Article; Review
Journal Info: Publisher: Springer-Verlag Italia Country of Publication: Italy NLM ID: 100959175 Publication Model: Electronic Cited Medium: Internet ISSN: 1590-3478 (Electronic) Linking ISSN: 15901874 NLM ISO Abbreviation: Neurol Sci Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Asymmetrical muscular disorder with normal creatine kinase (CK) and electromyography (EMG): the challenging diagnosis of muscular polyarteritis nodosa (MPAN), case report and literature review.
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  Data: <searchLink fieldCode="AU" term="%22Dib+A%22">Dib A</searchLink>; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France. alexandre.dib@chu-lyon.fr.; Service ENMG Et de Pathologies Neuromusculaires, Centre de Référence Des Maladies Neuromusculaires PACA-Réunion-Rhône Alpes, Hôpital Neurologique P. Wertheimer, Hospices Civils de Lyon, Bron, France. alexandre.dib@chu-lyon.fr.<br /><searchLink fieldCode="AU" term="%22Lequain+H%22">Lequain H</searchLink>; Department of Internal Medicine, Centre de Référence Des Maladies Auto-Inflammatoires Et de L'Amylose Inflammatoire (CéRéMAIA), Hôpital de La Croix-Rousse, Hospices Civils de Lyon, Université Claude-Bernard Lyon 1, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Fenouil+T%22">Fenouil T</searchLink>; Institute of Pathology - East Site, Groupement Hospitalier Est, Hospices Civils de Lyon, Bron, France.<br /><searchLink fieldCode="AU" term="%22Pegat+A%22">Pegat A</searchLink>; Service ENMG Et de Pathologies Neuromusculaires, Centre de Référence Des Maladies Neuromusculaires PACA-Réunion-Rhône Alpes, Hôpital Neurologique P. Wertheimer, Hospices Civils de Lyon, Bron, France.<br /><searchLink fieldCode="AU" term="%22Petiot+P%22">Petiot P</searchLink>; Service ENMG Et de Pathologies Neuromusculaires, Centre de Référence Des Maladies Neuromusculaires PACA-Réunion-Rhône Alpes, Hôpital Neurologique P. Wertheimer, Hospices Civils de Lyon, Bron, France.<br /><searchLink fieldCode="AU" term="%22Barta+A%22">Barta A</searchLink>; Department of Diagnostic and Interventional Radiology, Hôpital Edouard Herriot, Hospices Civils de Lyon, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Mayard+C%22">Mayard C</searchLink>; Department of Diagnostic and Interventional Radiology, Hôpital Edouard Herriot, Hospices Civils de Lyon, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Balletti+A%22">Balletti A</searchLink>; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Virot+E%22">Virot E</searchLink>; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.; Constitutive Reference Center, Major Sickle Cell Syndromes, Thalassemia and Other Rare Pathologies of Red Blood Cell and Erythropoiesis, Edouard Herriot Hospital, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Pascu+I%22">Pascu I</searchLink>; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Hot+A%22">Hot A</searchLink>; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.; Constitutive Reference Center, Major Sickle Cell Syndromes, Thalassemia and Other Rare Pathologies of Red Blood Cell and Erythropoiesis, Edouard Herriot Hospital, Lyon, France.<br /><searchLink fieldCode="AU" term="%22Gallay+L%22">Gallay L</searchLink>; Department of Internal Medicine and Clinical Immunology, Edouard Herriot University Hospital, Hospices Civils de Lyon, University Claude Bernard, Lyon, France.; Institut NeuroMyoGène, Laboratoire Physiopathologie Et Génétique du Neurone Et du Muscle, CNRS UMR 5261 - Inserm U1315, Université Claude Bernard Lyon 1, Lyon, France.
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