Polyglycine-mediated aggregation of FAM98B disrupts tRNA processing in GGC repeat disorders.

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Title: Polyglycine-mediated aggregation of FAM98B disrupts tRNA processing in GGC repeat disorders.
Authors: Yang, Jason1, Xu, Yunhan1, Ziehr, David R.1,2,3, Taylor, Martin S.4, Valenstein, Max L.1,2,3, Frenkel, Evgeni M.5, Bush, Jack R.1, Rutter, Kate1, Stevanovski, Igor6,7, Shi, Charlie Y.8,9,10, Kesavan, Maheswaran1,11, Pinto, Ricardo Mouro1,2,12, Deveson, Ira6,7,13, Bartel, David P.8,9,10, Sabatini, David M.5, Chivukula, Raghu R.1,2,3,14,15 rchivukula@mgh.harvard.edu
Source: Science. 7/17/2025, Vol. 389 Issue 6757, p1-20. 20p.
Database: Academic Search Ultimate
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ISSN:00368075
DOI:10.1126/science.ado2403