Polyglycine-mediated aggregation of FAM98B disrupts tRNA processing in GGC repeat disorders.
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| Title: | Polyglycine-mediated aggregation of FAM98B disrupts tRNA processing in GGC repeat disorders. |
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| Authors: | Yang, Jason1, Xu, Yunhan1, Ziehr, David R.1,2,3, Taylor, Martin S.4, Valenstein, Max L.1,2,3, Frenkel, Evgeni M.5, Bush, Jack R.1, Rutter, Kate1, Stevanovski, Igor6,7, Shi, Charlie Y.8,9,10, Kesavan, Maheswaran1,11, Pinto, Ricardo Mouro1,2,12, Deveson, Ira6,7,13, Bartel, David P.8,9,10, Sabatini, David M.5, Chivukula, Raghu R.1,2,3,14,15 rchivukula@mgh.harvard.edu |
| Source: | Science. 7/17/2025, Vol. 389 Issue 6757, p1-20. 20p. |
| Database: | Academic Search Ultimate |
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| FullText | Links: – Type: pdflink Text: Availability: 1 |
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| Header | DbId: asn DbLabel: Academic Search Ultimate An: 188103302 AccessLevel: 2 PubType: Academic Journal PubTypeId: academicJournal PreciseRelevancyScore: 0 |
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| PLink | https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=asn&AN=188103302 |
| RecordInfo | BibRecord: BibEntity: Identifiers: – Type: doi Value: 10.1126/science.ado2403 Languages: – Code: eng Text: English PhysicalDescription: Pagination: PageCount: 20 StartPage: 1 Titles: – TitleFull: Polyglycine-mediated aggregation of FAM98B disrupts tRNA processing in GGC repeat disorders. Type: main BibRelationships: HasContributorRelationships: – PersonEntity: Name: NameFull: Yang, Jason – PersonEntity: Name: NameFull: Xu, Yunhan – PersonEntity: Name: NameFull: Ziehr, David R. – PersonEntity: Name: NameFull: Taylor, Martin S. – PersonEntity: Name: NameFull: Valenstein, Max L. – PersonEntity: Name: NameFull: Frenkel, Evgeni M. – PersonEntity: Name: NameFull: Bush, Jack R. – PersonEntity: Name: NameFull: Rutter, Kate – PersonEntity: Name: NameFull: Stevanovski, Igor – PersonEntity: Name: NameFull: Shi, Charlie Y. – PersonEntity: Name: NameFull: Kesavan, Maheswaran – PersonEntity: Name: NameFull: Pinto, Ricardo Mouro – PersonEntity: Name: NameFull: Deveson, Ira – PersonEntity: Name: NameFull: Bartel, David P. – PersonEntity: Name: NameFull: Sabatini, David M. – PersonEntity: Name: NameFull: Chivukula, Raghu R. IsPartOfRelationships: – BibEntity: Dates: – D: 17 M: 07 Text: 7/17/2025 Type: published Y: 2025 Identifiers: – Type: issn-print Value: 00368075 Numbering: – Type: volume Value: 389 – Type: issue Value: 6757 Titles: – TitleFull: Science Type: main |
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