Tetrahydrobiopterin treatment reduces brain L-Phe but only partially improves serotonin in hyperphenylalaninemic ENU1/2 mice.

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Title: Tetrahydrobiopterin treatment reduces brain L-Phe but only partially improves serotonin in hyperphenylalaninemic ENU1/2 mice.
Authors: Scherer T; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland., Allegri G; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland., Sarkissian CN; Department of Biology, McGill University, Montreal, QC, H3A 1B1, Canada., Ying M; Department of Biomedicine and K.G. Jebsen Centre for Neuropsychiatric Disorders, University of Bergen, Bergen, Norway., Grisch-Chan HM; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland., Rassi A; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland., Winn SR; Department of Molecular and Medical Genetics, School of Medicine, Oregon Science & Health University, Portland, OR, USA., Harding CO; Department of Molecular and Medical Genetics, School of Medicine, Oregon Science & Health University, Portland, OR, USA., Martinez A; Department of Biomedicine and K.G. Jebsen Centre for Neuropsychiatric Disorders, University of Bergen, Bergen, Norway. aurora.martinez@uib.no., Thöny B; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland. beat.thony@kispi.uzh.ch.
Source: Journal of inherited metabolic disease [J Inherit Metab Dis] 2018 Jul; Vol. 41 (4), pp. 709-718. Date of Electronic Publication: 2018 Mar 08.
Publication Type: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
Journal Info: Publisher: Wiley Country of Publication: United States NLM ID: 7910918 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1573-2665 (Electronic) Linking ISSN: 01418955 NLM ISO Abbreviation: J Inherit Metab Dis Subsets: MEDLINE
Database: MEDLINE Ultimate
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  Data: Tetrahydrobiopterin treatment reduces brain L-Phe but only partially improves serotonin in hyperphenylalaninemic ENU1/2 mice.
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  Data: <searchLink fieldCode="AU" term="%22Scherer+T%22">Scherer T</searchLink>; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland.<br /><searchLink fieldCode="AU" term="%22Allegri+G%22">Allegri G</searchLink>; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland.<br /><searchLink fieldCode="AU" term="%22Sarkissian+CN%22">Sarkissian CN</searchLink>; Department of Biology, McGill University, Montreal, QC, H3A 1B1, Canada.<br /><searchLink fieldCode="AU" term="%22Ying+M%22">Ying M</searchLink>; Department of Biomedicine and K.G. Jebsen Centre for Neuropsychiatric Disorders, University of Bergen, Bergen, Norway.<br /><searchLink fieldCode="AU" term="%22Grisch-Chan+HM%22">Grisch-Chan HM</searchLink>; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland.<br /><searchLink fieldCode="AU" term="%22Rassi+A%22">Rassi A</searchLink>; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland.<br /><searchLink fieldCode="AU" term="%22Winn+SR%22">Winn SR</searchLink>; Department of Molecular and Medical Genetics, School of Medicine, Oregon Science & Health University, Portland, OR, USA.<br /><searchLink fieldCode="AU" term="%22Harding+CO%22">Harding CO</searchLink>; Department of Molecular and Medical Genetics, School of Medicine, Oregon Science & Health University, Portland, OR, USA.<br /><searchLink fieldCode="AU" term="%22Martinez+A%22">Martinez A</searchLink>; Department of Biomedicine and K.G. Jebsen Centre for Neuropsychiatric Disorders, University of Bergen, Bergen, Norway. aurora.martinez@uib.no.<br /><searchLink fieldCode="AU" term="%22Thöny+B%22">Thöny B</searchLink>; Department of Pediatrics, Divisions of Metabolism and of Clinical Chemistry and Biochemistry, University of Zürich, Zürich, Switzerland. beat.thony@kispi.uzh.ch.
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  Data: <searchLink fieldCode="JN" term="%227910918%22">Journal of inherited metabolic disease</searchLink> [J Inherit Metab Dis] 2018 Jul; Vol. 41 (4), pp. 709-718. <i>Date of Electronic Publication: </i>2018 Mar 08.
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  Data: Journal Article; Research Support, N.I.H., Extramural; Research Support, Non-U.S. Gov't
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  Data: <i>Publisher: </i><searchLink fieldCode="PB" term="%22Wiley%22">Wiley </searchLink><i>Country of Publication: </i>United States <i>NLM ID: </i>7910918 <i>Publication Model: </i>Print-Electronic <i>Cited Medium: </i>Internet <i>ISSN: </i>1573-2665 (Electronic) <i>Linking ISSN: </i><searchLink fieldCode="IS" term="%2201418955%22">01418955 </searchLink><i>NLM ISO Abbreviation: </i>J Inherit Metab Dis <i>Subsets: </i>MEDLINE
PLink https://search.ebscohost.com/login.aspx?direct=true&site=eds-live&db=mdl&AN=29520738
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        Value: 10.1007/s10545-018-0150-y
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      – TitleFull: Tetrahydrobiopterin treatment reduces brain L-Phe but only partially improves serotonin in hyperphenylalaninemic ENU1/2 mice.
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              Text: 2018 Jul
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