Longitudinal Monitoring of Lumacaftor/Ivacaftor Response in Young Children with Cystic Fibrosis Lung Disease Using 129Xe MRI.

Saved in:
Bibliographic Details
Title: Longitudinal Monitoring of Lumacaftor/Ivacaftor Response in Young Children with Cystic Fibrosis Lung Disease Using 129Xe MRI.
Authors: Bdaiwi AS; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.)., Roach DJ; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.)., West ME; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.)., Willmering MM; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.); Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.W., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.)., Daou AW; Division of Pulmonary and Sleep Medicine, Children's Hospital of Philadelphia, Philadelphia, Pennsylvania (A.W.D.)., Hossain MM; Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio (M.M.H., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Department of Biostatistics and Epidemiology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.H.)., Kramer EL; Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio (M.M.H., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.W., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.)., Amin R; Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio (M.M.H., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.W., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.)., Walkup LL; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.); Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio (M.M.H., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.W., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Department of Radiology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (L.L.W., Z.I.C., J.C.W.)., Cleveland ZI; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.); Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio (M.M.H., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.W., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Department of Radiology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (L.L.W., Z.I.C., J.C.W.)., Woods JC; Center for Pulmonary Imaging Research, Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (A.S.B., D.J.R., M.E.W., M.M.W., L.L.W., Z.I.C., J.C.W.); Department of Pediatrics, University of Cincinnati College of Medicine, Cincinnati, Ohio (M.M.H., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Division of Pulmonary Medicine, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (M.M.W., E.L.K., R.A., L.L.W., Z.I.C., J.C.W.); Department of Radiology, Cincinnati Children's Hospital Medical Center, Cincinnati, Ohio (L.L.W., Z.I.C., J.C.W.). Electronic address: Jason.Woods@cchmc.org.
Source: Academic radiology [Acad Radiol] 2025 Oct; Vol. 32 (10), pp. 6238-6249. Date of Electronic Publication: 2025 Jul 10.
Publication Type: Journal Article
Journal Info: Publisher: Association Of University Radiologists Country of Publication: United States NLM ID: 9440159 Publication Model: Print-Electronic Cited Medium: Internet ISSN: 1878-4046 (Electronic) Linking ISSN: 10766332 NLM ISO Abbreviation: Acad Radiol Subsets: MEDLINE
Database: MEDLINE Ultimate
Description
ISSN:1878-4046
DOI:10.1016/j.acra.2025.06.042