Rare SRY-negative 46,XX disorder of sex development with male phenotype and ectopic gonads: a case report.

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Title: Rare SRY-negative 46,XX disorder of sex development with male phenotype and ectopic gonads: a case report.
Authors: Luo J; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Huang F; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Li J; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Mo E; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Wang H; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Zhang J; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Pang C; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Lei D; Department of General Surgery, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China., Chen J; Department of Urology, Maternal and Child Health Hospital of Guangxi Zhuang Autonomous Region, Nanning, China.
Source: Frontiers in endocrinology [Front Endocrinol (Lausanne)] 2026 Apr 30; Vol. 17, pp. 1829751. Date of Electronic Publication: 2026 Apr 30 (Print Publication: 2026).
Publication Type: Case Reports; Journal Article
Journal Info: Publisher: Frontiers Research Foundation] Country of Publication: Switzerland NLM ID: 101555782 Publication Model: eCollection Cited Medium: Print ISSN: 1664-2392 (Print) Linking ISSN: 16642392 NLM ISO Abbreviation: Front Endocrinol (Lausanne) Subsets: MEDLINE
Database: MEDLINE Ultimate
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ISSN:1664-2392
DOI:10.3389/fendo.2026.1829751